Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report

SARILAR, Caner; ERDEM, Atilla; Leventoglu, Alev; Cansu, Ali; acik, vedat

Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report

Atilla ERDEM, (Ankara Üniversitesi, Tıp Fakültesi, Nöroşirürji Anabilim Dalı, Ankara, Türkiye)

Vedat AÇIK, (Ankara Üniversitesi, Tıp Fakültesi, Nöroşirürji Anabilim Dalı, Ankara, Türkiye)

Alev LEVENTOĞLU, (Ufuk Üniversitesi, Tıp Fakültesi, Nöroşirürji Anabilim Dalı, Ankara, Türkiye)

Caner SARILAR, (Ankara Üniversitesi, Tıp Fakültesi, Nöroşirürji Anabilim Dalı, Ankara, Türkiye)

Ali CANSU (Karadeniz Teknik Üniversitesi, Tıp Fakültesi, Pediatri Anabilim Dalı, Trabzon, Türkiye)

Turkish Neurosurgery

1 0

Yıl: 2009 Cilt: 19 Sayı: 2 Sayfa Aralığı: 197 - 199 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report

Öz:

Bu yazımızda Dyke-Davidoff-Masson sendromu (DDMS) olup sol vagal sinir stimulatörü ile belirgin şekilde nöbetleri azalan (Engel grade III) 20 yaşında kadın hastayı sunduk. Özgeçmişinden forseps yardımı ile zor doğum öyküsü alındı. DDMS tanısı olan hastanın 4 yaşında başlayan ilaca dirençli epilepsi öyküsü mevcuttu. Mental retardasyon tespit edilmedi. Altı yıldır 3'lü antiepileptik ilaç tedavisi almasına rağmen nöbetleri devam etmekteydi. Hastaya soldan vagal sinir stimülatörü takıldı. Postoperatif dönemde hastanın nöbet frekansı ve şiddetinde anlamlı düzelme kaydedildi. Bu vaka ile, DDMS'na bağlı ilaca dirençli epilepsilerde vagal sinir stimülasyonunun, geniş lezyonektomilere önemli bir alternatif olabileceği vurgulanmak istenmiştir. İncelenebildiği kadarı ile bu vaka, medikal literatürde vagal sinir stimülatörü kullanılarak nöbetleri anlamlı ölçüde kontrol edilebilen ilk DDMS vakasıdır.

Anahtar Kelime:

Konular: Cerrahi

Dyke-davidoff-masson sendromuna bağlı refrakter generalize epilepside vagal sinir stimülasyonunun etkisi

Öz:

We report a case of Dyke–Davidoff–Masson syndrome (DDMS) in whom left vagal nerve stimulation (VNS) resulted in worthwhile seizure reduction (Engel's Classification Class III). A 20-year-old woman with DDMS whose seizures were medically intractable was successfully treated using left VNS. She was born at term by unsuccessful forceps-assisted vaginal delivery. Her seizures started at the age of 4. There was no detectable mental retardation. Her seizures were intractable although she had been receiving three medications for sixteen years. She underwent left vagal nerve stimulator placement. Pre-stimulation seizure frequency was three seizures per month. This case shows that VNS is an alternative treatment procedure for medically intractable seizures in DDMS. To our knowledge, this is the first case in the world literature reporting worthwhile seizure reduction in DDMS after VNS.

Anahtar Kelime:

Konular: Cerrahi

Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık

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APA	ERDEM A, acik v, Leventoglu A, SARILAR C, Cansu A (2009). Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. , 197 - 199.
Chicago	ERDEM Atilla,acik vedat,Leventoglu Alev,SARILAR Caner,Cansu Ali Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. (2009): 197 - 199.
MLA	ERDEM Atilla,acik vedat,Leventoglu Alev,SARILAR Caner,Cansu Ali Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. , 2009, ss.197 - 199.
AMA	ERDEM A,acik v,Leventoglu A,SARILAR C,Cansu A Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. . 2009; 197 - 199.
Vancouver	ERDEM A,acik v,Leventoglu A,SARILAR C,Cansu A Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. . 2009; 197 - 199.
IEEE	ERDEM A,acik v,Leventoglu A,SARILAR C,Cansu A "Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report." , ss.197 - 199, 2009.
ISNAD	ERDEM, Atilla vd. "Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report". (2009), 197-199.

APA	ERDEM A, acik v, Leventoglu A, SARILAR C, Cansu A (2009). Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. Turkish Neurosurgery, 19(2), 197 - 199.
Chicago	ERDEM Atilla,acik vedat,Leventoglu Alev,SARILAR Caner,Cansu Ali Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. Turkish Neurosurgery 19, no.2 (2009): 197 - 199.
MLA	ERDEM Atilla,acik vedat,Leventoglu Alev,SARILAR Caner,Cansu Ali Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. Turkish Neurosurgery, vol.19, no.2, 2009, ss.197 - 199.
AMA	ERDEM A,acik v,Leventoglu A,SARILAR C,Cansu A Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. Turkish Neurosurgery. 2009; 19(2): 197 - 199.
Vancouver	ERDEM A,acik v,Leventoglu A,SARILAR C,Cansu A Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report. Turkish Neurosurgery. 2009; 19(2): 197 - 199.
IEEE	ERDEM A,acik v,Leventoglu A,SARILAR C,Cansu A "Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report." Turkish Neurosurgery, 19, ss.197 - 199, 2009.
ISNAD	ERDEM, Atilla vd. "Effect of vagal nerve stimulation in dyke–davidoff–masson syndrome with refractory generalized seizures – case report". Turkish Neurosurgery 19/2 (2009), 197-199.