Anesthetic management of a patient with beckwith-wiedemann syndrome

DOĞAN BAKI, ELİF; KARSLI, Bilge; ÜNAL, Ceyda; ÖZTÜRK KAVRUT, Nilgün; ÇELİK, Mehmet Ümit

Anesthetic management of a patient with beckwith-wiedemann syndrome

ELİF DOĞAN BAKI, (Afyon Kocatepe Üniversitesi, Tıp Fakültesi, Anesteziyoloji Anabilim Dalı, Afyon, Türkiye)

Ceyda ÜNAL, (Sağlık Bakanlığı, Antalya Eğitim ve Araştırma Hastanesi, Anesteziyoloji ve Reanimasyon Kliniği, Antalya, Türkiye)

Nilgün ÖZTÜRK KAVRUT, (Sağlık Bakanlığı, Antalya Eğitim ve Araştırma Hastanesi, Anesteziyoloji ve Reanimasyon Kliniği, Antalya, Türkiye)

Mehmet Ümit ÇELİK, (Sağlık Bakanlığı, Antalya Eğitim ve Araştırma Hastanesi, Anesteziyoloji ve Reanimasyon Kliniği, Antalya, Türkiye)

Bilge KARSLI (Akdeniz Üniversitesi, Tıp Fakültesi, Anesteziyoloji Anabilim Dalı, Antalya, Türkiye)

Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi

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Yıl: 2013 Cilt: 14 Sayı: 1 Sayfa Aralığı: 48 - 50 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Anesthetic management of a patient with beckwith-wiedemann syndrome

Öz:

Beckwith-Widemann sendromu (BWS) neonatal periyotta yaklaşık 13700 canlı doğumda 1 görülür. Bu sendrom makroglossi, omfalosel, viseromegali, gigantism, neonatal hipoglisemi gibi birçok anomaliler içerir. Havayolu yöneti- mini makroglossinin sebep olabileceği zor ventilasyon ve endotrakeal entubasyonun komplike hale getirmesi bekle- nir. Bu yüzden anestezi induksiyonu öncesi zor havayolu hazırlığı düşünülmelidir. BWSda diğer bir problemde postoperatif analjezidir. Çünkü opioid kullanımı solunumu deprese edebilkirken, non- steroid antiinflamatuar ilaçlarda kanamaya yol açabilece- ğinden postoperatif analjezi yönetimi dikkatlice planlanma- lıdır. Biz büyük bir dile sahip, adenotonsillektomi ameliyatı yapı- lacak 8 yaşında Beckwith-Widemann sendromlu hastada anestezi yönetimini sunduk.

Anahtar Kelime:

Konular: Genel ve Dahili Tıp

Beckwith-wiedemann sendromlu hastada anestezi yönetimi

Öz:

Beckwith-Widemann Syndrome (BWS) occurs in the neona- tal period at a frequency of approximately one in 13 700 live births. This syndrome consists of abnormalities, such as; macroglossia, omphalocele, visceromegaly, gigantism and neonatal hypoglycemia. It is expected that airway management would be complicated by macroglossia which might cause difficult ventilation and endotracheal intuba- tion. Therefore preparations for airway difficulty should be considered before anesthesia induction. Another problem in BWS is postoperative analgesia. Be- cause opioids can depress breathing and non steroid anti- inflammatory drugs can increase bleeding, postoperative analgesia should be planned carefully. We present anesthetic management of an eight years old patient with BWS having big tongue undergoing tonsil- adenoid resection.

Anahtar Kelime:

Konular: Genel ve Dahili Tıp

Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık

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APA	DOĞAN BAKI E, ÜNAL C, ÖZTÜRK KAVRUT N, ÇELİK M, KARSLI B (2013). Anesthetic management of a patient with beckwith-wiedemann syndrome. , 48 - 50.
Chicago	DOĞAN BAKI ELİF,ÜNAL Ceyda,ÖZTÜRK KAVRUT Nilgün,ÇELİK Mehmet Ümit,KARSLI Bilge Anesthetic management of a patient with beckwith-wiedemann syndrome. (2013): 48 - 50.
MLA	DOĞAN BAKI ELİF,ÜNAL Ceyda,ÖZTÜRK KAVRUT Nilgün,ÇELİK Mehmet Ümit,KARSLI Bilge Anesthetic management of a patient with beckwith-wiedemann syndrome. , 2013, ss.48 - 50.
AMA	DOĞAN BAKI E,ÜNAL C,ÖZTÜRK KAVRUT N,ÇELİK M,KARSLI B Anesthetic management of a patient with beckwith-wiedemann syndrome. . 2013; 48 - 50.
Vancouver	DOĞAN BAKI E,ÜNAL C,ÖZTÜRK KAVRUT N,ÇELİK M,KARSLI B Anesthetic management of a patient with beckwith-wiedemann syndrome. . 2013; 48 - 50.
IEEE	DOĞAN BAKI E,ÜNAL C,ÖZTÜRK KAVRUT N,ÇELİK M,KARSLI B "Anesthetic management of a patient with beckwith-wiedemann syndrome." , ss.48 - 50, 2013.
ISNAD	DOĞAN BAKI, ELİF vd. "Anesthetic management of a patient with beckwith-wiedemann syndrome". (2013), 48-50.

APA	DOĞAN BAKI E, ÜNAL C, ÖZTÜRK KAVRUT N, ÇELİK M, KARSLI B (2013). Anesthetic management of a patient with beckwith-wiedemann syndrome. Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi, 14(1), 48 - 50.
Chicago	DOĞAN BAKI ELİF,ÜNAL Ceyda,ÖZTÜRK KAVRUT Nilgün,ÇELİK Mehmet Ümit,KARSLI Bilge Anesthetic management of a patient with beckwith-wiedemann syndrome. Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi 14, no.1 (2013): 48 - 50.
MLA	DOĞAN BAKI ELİF,ÜNAL Ceyda,ÖZTÜRK KAVRUT Nilgün,ÇELİK Mehmet Ümit,KARSLI Bilge Anesthetic management of a patient with beckwith-wiedemann syndrome. Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi, vol.14, no.1, 2013, ss.48 - 50.
AMA	DOĞAN BAKI E,ÜNAL C,ÖZTÜRK KAVRUT N,ÇELİK M,KARSLI B Anesthetic management of a patient with beckwith-wiedemann syndrome. Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi. 2013; 14(1): 48 - 50.
Vancouver	DOĞAN BAKI E,ÜNAL C,ÖZTÜRK KAVRUT N,ÇELİK M,KARSLI B Anesthetic management of a patient with beckwith-wiedemann syndrome. Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi. 2013; 14(1): 48 - 50.
IEEE	DOĞAN BAKI E,ÜNAL C,ÖZTÜRK KAVRUT N,ÇELİK M,KARSLI B "Anesthetic management of a patient with beckwith-wiedemann syndrome." Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi, 14, ss.48 - 50, 2013.
ISNAD	DOĞAN BAKI, ELİF vd. "Anesthetic management of a patient with beckwith-wiedemann syndrome". Afyon Kocatepe Üniversitesi Kocatepe Tıp Dergisi 14/1 (2013), 48-50.