Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report
Yıl: 2013 Cilt: 28 Sayı: 1 Sayfa Aralığı: 58 - 61 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022
Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report
Öz: Bu olgu sunumunda şiddetli hipokaleminin ortaya çıkardığı distal renal tübüler asidoz (RTA) ve normal anyon boşluk metabolik asidozu ve anormal düzeyde asitleşmiş idrar ile birlikte seyreden primer Sjogren sendromlu (pSS) 75 yaşındaki bir kadın olgu sunuldu. Hastada kuadripleji, hipersomnia ve disfaji ile doğrulanmış beyinsapı lezyonu mevcuttu. Laboratuvar testlerinde anti-Ro/SS-A ve anti-La/SS-B antikorları pozitifti. Manyetik rezonans görüntüleme ile yapılan beyin taramasında, santral pontin miyelinolizisin tipik özelliği olan orta ponlarda T1 ve T2'de hiperintens sinyal görüldü
Anahtar Kelime: Konular:
Renal Tübüler Asidoz ve Santral Pontin Miyelinolizis ile Seyreden Primer Sjogren Sendromu: Olgu Sunumu
Öz: In this case report, we present a-75-year-old female case of primary Sjogren's syndrome (pSS) with distal renal tubular acidosis (RTA) as revealed by severe hypokalemia along with normal anion gap metabolic acidosis and abnormally acidified urine. The patient had a brain stem lesion as confirmed by quadriplegia, hypersomnia, and dysphagia. Laboratory tests revealed that the anti-Ro/SSA and anti-La/SSB antibodies were positive. Magnetic resonance imaging of the brain showed a hyperintense signal at T1 and T2 in the mid-pons, a typical characteristic of central pontine myelinolysis
Anahtar Kelime: Konular:
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
- Xiang YJ, Dai SM. Prevalence of rheumatic diseases and disability in China. Rheumatol Int 2009;29:481-90. doi: 10.1007/s00296-008-0809-z.
- Vitali C, Bombardieri S, Jonsson R, Moutsopoulos HM, Alexander EL, Carsons SE, et al. Classification criteria for Sjögren's syndrome: a revised version of the European criteria proposed by the American-European Consensus Group. Ann Rheum Dis 2002;61:554-8.
- Yoon KH, Fong KY, Koh DR, Suri R. Central pontine myelinolysis-a rare manifestation of CNS Sjogren's syndrome. Lupus 2000;9:471-3.
- Deleu D, Salim K, Mesraoua B, El Siddig A, Al Hail H, Hanssens Y. "Man-in-the-barrel" syndrome as delayed manifestation of extrapontine and central pontine myelinolysis: beneficial effect of intravenous immunoglobulin. J Neurol Sci 2005;237:103-6.
- Baburaj P, Khanna L. Secondary Sjogren's syndrome and scleroderma presenting as renal tubular acidosis. J Assoc Physicians India 2007;55:78-9.
- Lin DF, Yan SM, Zhao Y, Zhang W, Li MT, Zeng XF, et al. Clinical and prognostic characteristics of 573 cases of primary Sjögren's syndrome. Chin Med J (Engl) 2010;123:3252-7.
- Lerma EV, Berns JS, Nissenson AR, editors. Current diagnosis & treatment: nephrology & hypertension. New York: McGraw Hill Companies; 2009.
- Bossini N, Savoldi S, Franceschini F, Mombelloni S, Baronio M, Cavazzana I, et al. Clinical and morphological features of kidney involvement in primary Sjögren's syndrome. Nephrol Dial Transplant 2001;16:2328-36.
| APA | RUBO S, ZHANG L (2013). Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. , 58 - 61. |
| Chicago | RUBO Sui,ZHANG Lei Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. (2013): 58 - 61. |
| MLA | RUBO Sui,ZHANG Lei Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. , 2013, ss.58 - 61. |
| AMA | RUBO S,ZHANG L Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. . 2013; 58 - 61. |
| Vancouver | RUBO S,ZHANG L Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. . 2013; 58 - 61. |
| IEEE | RUBO S,ZHANG L "Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report." , ss.58 - 61, 2013. |
| ISNAD | RUBO, Sui - ZHANG, Lei. "Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report". (2013), 58-61. |
| APA | RUBO S, ZHANG L (2013). Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. Turkish Journal of Rheumatology(.)Archives of Rheumatology, 28(1), 58 - 61. |
| Chicago | RUBO Sui,ZHANG Lei Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. Turkish Journal of Rheumatology(.)Archives of Rheumatology 28, no.1 (2013): 58 - 61. |
| MLA | RUBO Sui,ZHANG Lei Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. Turkish Journal of Rheumatology(.)Archives of Rheumatology, vol.28, no.1, 2013, ss.58 - 61. |
| AMA | RUBO S,ZHANG L Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. Turkish Journal of Rheumatology(.)Archives of Rheumatology. 2013; 28(1): 58 - 61. |
| Vancouver | RUBO S,ZHANG L Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report. Turkish Journal of Rheumatology(.)Archives of Rheumatology. 2013; 28(1): 58 - 61. |
| IEEE | RUBO S,ZHANG L "Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report." Turkish Journal of Rheumatology(.)Archives of Rheumatology, 28, ss.58 - 61, 2013. |
| ISNAD | RUBO, Sui - ZHANG, Lei. "Primary Sjogren's Syndrome Presenting with Renal Tubular Acidosis and Central Pontine Myelinolysis: A Case Report". Turkish Journal of Rheumatology(.)Archives of Rheumatology 28/1 (2013), 58-61. |
