Yıl: 2014 Cilt: 1 Sayı: 1 Sayfa Aralığı: 21 - 33 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Familial Mediterranean fever: An updated review

Öz:
Ailevi Akdeniz ateşi (AAA) akut ateş atakları ve serozal inflamasyonla karakterize kalıtsal otoinflamatuvar bir bozukluktur. AAA öncelikle Yahudi, Ermeni, Türk ve Arap popülasyonlarını etkiler. Hastalığa atakların ve ataksız dönemlerdeki subklinik inflamasyonun etkileri nedeniyle oluşan yaşam kalitesindeki belirgin düşüş eşlik eder. Tedavi edilmemiş veya yetersiz tedavi edilmiş hastalar morbiditenin ve mortalitenin önemli bir nedeni olan amiloidoz riski taşır. Bu derlemede, AAA üzerine mevcut bilgiler özetlendi.
Anahtar Kelime:

Konular: Romatoloji

Ailevi Akdeniz Ateşi: Güncellenmiş derleme

Öz:
Familial Mediterranean Fever (FMF) is a hereditary autoinflammatory disorder characterised by acute attacks of fever and serosal inflammation. FMF primarily affects Jewish, Armenian, Turkish, and Arab populations. The disease is accompanied by a marked decrease in quality of life due to the effects of attacks and subclinical inflammation in the attack-free periods. Untreated or inadequately treated patients run the risk of amyloidosis, which is an important cause of morbidity and mortality. In this review, the current information available on FMF is summarised
Anahtar Kelime:

Konular: Romatoloji
Belge Türü: Makale Makale Türü: Derleme Erişim Türü: Erişime Açık
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APA Sari I, Birlik M, KAŞİFOĞLU T (2014). Familial Mediterranean fever: An updated review. , 21 - 33.
Chicago Sari Ismail,Birlik Merih,KAŞİFOĞLU Timuçin Familial Mediterranean fever: An updated review. (2014): 21 - 33.
MLA Sari Ismail,Birlik Merih,KAŞİFOĞLU Timuçin Familial Mediterranean fever: An updated review. , 2014, ss.21 - 33.
AMA Sari I,Birlik M,KAŞİFOĞLU T Familial Mediterranean fever: An updated review. . 2014; 21 - 33.
Vancouver Sari I,Birlik M,KAŞİFOĞLU T Familial Mediterranean fever: An updated review. . 2014; 21 - 33.
IEEE Sari I,Birlik M,KAŞİFOĞLU T "Familial Mediterranean fever: An updated review." , ss.21 - 33, 2014.
ISNAD Sari, Ismail vd. "Familial Mediterranean fever: An updated review". (2014), 21-33.
APA Sari I, Birlik M, KAŞİFOĞLU T (2014). Familial Mediterranean fever: An updated review. European Journal of Rheumatology, 1(1), 21 - 33.
Chicago Sari Ismail,Birlik Merih,KAŞİFOĞLU Timuçin Familial Mediterranean fever: An updated review. European Journal of Rheumatology 1, no.1 (2014): 21 - 33.
MLA Sari Ismail,Birlik Merih,KAŞİFOĞLU Timuçin Familial Mediterranean fever: An updated review. European Journal of Rheumatology, vol.1, no.1, 2014, ss.21 - 33.
AMA Sari I,Birlik M,KAŞİFOĞLU T Familial Mediterranean fever: An updated review. European Journal of Rheumatology. 2014; 1(1): 21 - 33.
Vancouver Sari I,Birlik M,KAŞİFOĞLU T Familial Mediterranean fever: An updated review. European Journal of Rheumatology. 2014; 1(1): 21 - 33.
IEEE Sari I,Birlik M,KAŞİFOĞLU T "Familial Mediterranean fever: An updated review." European Journal of Rheumatology, 1, ss.21 - 33, 2014.
ISNAD Sari, Ismail vd. "Familial Mediterranean fever: An updated review". European Journal of Rheumatology 1/1 (2014), 21-33.