Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome

KABAKOĞLU ÜNSÜR, EMEL; Pac Kisaarslan, Aysenur; sozeri, betul

Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome

Ayşenur Paç KISAARSLAN, (University of Health Sciences, Ümraniye Training and Research Hospital, Clinic of Pediatric Rheumatology, İstanbul, Turkey)

Emel Kabakoğlu ÜNSÜR, (Erciyes University Faculty of Medicine, Department of Pediatrics, Division of Pediatric Nephrology, Kayseri, Turkey)

Betül SÖZERİ (University of Health Sciences, Ümraniye Training and Research Hospital, Clinic of Pediatric Rheumatology, İstanbul, Turkey)

The Journal of Pediatric Research

1 0

Yıl: 2017 Cilt: 4 Sayı: 2 Sayfa Aralığı: 42 - 45 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome

Öz:

Periyodik ateş, aftöz stomatit, farenjit ve servikal lenfadenit (PFAPA) sendromu çocukluk çağında görülen, en sık tekrarlayan ateş nedenidir. PFAPA patogenezi halen tam olarak bilinmemektedir. Siklik nötropeni ve diğer monogenik otoenflamatuvar hastalıklarla ayırıcı tanısının yapılması gerekmektedir. Kendini sınırlayan ve benign bir hastalık olduğu için henüz netlik kazanmış bir tedavi şekli yoktur. Tedavi seçeneklerinin ise güçlü bir ebeveyn-doktor ilişkisi yardımıyla hastaya özel olarak seçilmesi gerekmektedir.

Anahtar Kelime:

Konular: Pediatri

Periyodik Ateş, Aftöz Stomatit, Farenjit ve Servikal Lenfadenit Sendromuna Güncel Tanı ve Tedavi Yaklaşımları

Öz:

Periodic fever, aphthous stomatitis, pharyngitis, and cervical lymphadenitis (PFAPA) syndrome is the most frequent cause of periodic fever in childhood. The pathogenesis of PFAPA is still unknown. Differantial diagnosis must be made with cyclic neutropenia and other autoinflammatory diseases. Because PFAPA is self limiting and benign, there is no certain treatment model. Treatment options must be specific to the patient, with a strong family and doctor relationship.

Anahtar Kelime:

Konular: Pediatri

Belge Türü: Makale Makale Türü: Derleme Erişim Türü: Erişime Açık

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APA	Pac Kisaarslan A, KABAKOĞLU ÜNSÜR E, sozeri b (2017). Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. , 42 - 45.
Chicago	Pac Kisaarslan Aysenur,KABAKOĞLU ÜNSÜR EMEL,sozeri betul Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. (2017): 42 - 45.
MLA	Pac Kisaarslan Aysenur,KABAKOĞLU ÜNSÜR EMEL,sozeri betul Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. , 2017, ss.42 - 45.
AMA	Pac Kisaarslan A,KABAKOĞLU ÜNSÜR E,sozeri b Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. . 2017; 42 - 45.
Vancouver	Pac Kisaarslan A,KABAKOĞLU ÜNSÜR E,sozeri b Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. . 2017; 42 - 45.
IEEE	Pac Kisaarslan A,KABAKOĞLU ÜNSÜR E,sozeri b "Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome." , ss.42 - 45, 2017.
ISNAD	Pac Kisaarslan, Aysenur vd. "Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome". (2017), 42-45.

APA	Pac Kisaarslan A, KABAKOĞLU ÜNSÜR E, sozeri b (2017). Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. The Journal of Pediatric Research, 4(2), 42 - 45.
Chicago	Pac Kisaarslan Aysenur,KABAKOĞLU ÜNSÜR EMEL,sozeri betul Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. The Journal of Pediatric Research 4, no.2 (2017): 42 - 45.
MLA	Pac Kisaarslan Aysenur,KABAKOĞLU ÜNSÜR EMEL,sozeri betul Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. The Journal of Pediatric Research, vol.4, no.2, 2017, ss.42 - 45.
AMA	Pac Kisaarslan A,KABAKOĞLU ÜNSÜR E,sozeri b Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. The Journal of Pediatric Research. 2017; 4(2): 42 - 45.
Vancouver	Pac Kisaarslan A,KABAKOĞLU ÜNSÜR E,sozeri b Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome. The Journal of Pediatric Research. 2017; 4(2): 42 - 45.
IEEE	Pac Kisaarslan A,KABAKOĞLU ÜNSÜR E,sozeri b "Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome." The Journal of Pediatric Research, 4, ss.42 - 45, 2017.
ISNAD	Pac Kisaarslan, Aysenur vd. "Current Diagnosis and Treatment Models of Periodic Fever, Aphthous Stomatitis, Pharyngitis and Cervical Lymphadenitis Syndrome". The Journal of Pediatric Research 4/2 (2017), 42-45.