Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement

Yilmaz, Osman; Doğan, Vehbi; karademir, selmin; ÖRÜN, Utku Arman; Ozgur, Senem; Keskin, Mahmut; CEYLAN, Özben; KOÇ, Murat

Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement

Özben CEYLAN, (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Senem ÖZGÜR, (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Utku Arman ÖRÜN, (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Vehbi DOĞAN, (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Murat KOÇ, (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Osman YILMAZ, (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Mahmut KESKİN, (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Selmin KARADEMİR (Dr. Sami Ulus Obstetrics and Gynecology, Children's Health and Diseases Training and Research Hospital, Ankara, Turkey)

Türk Göğüs Kalp Damar Cerrahisi Dergisi

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Yıl: 2014 Cilt: 22 Sayı: 1 Sayfa Aralığı: 7 - 12 Metin Dili: Türkçe İndeks Tarihi: 29-07-2022

Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement

Öz:

Amaç: Bu çalışmada koroner sinüsü geniş olan hastalarda büyük torasik venlerin dönüş anormalliklerini saptayabilmede ekokardiyografinin rolü araştırıldı.Çalışmaplanı:Ocak 2010 - Şubat 2012 tarihleri arasında kliniğimizde altı hastaya (3 erkek, 3 kız; ort. yaş 4.1; dağılım 3 gün - 9 yıl) kalıcı sol superior vena kavanın (SVK) eşlik ettiği sağ superior vena kava (SVK) yokluğu tanısı konuldu. Sağ SVC yokluğu tanısı ekokardiyografi ve anjiyografi ile konuldu.Bul gu lar: Dört hastada sağ SVK yokluğu tanısı ekokardiyografi ile teyit edildi. İki hastada ise, kardiyak kateterizasyon ve anjiyografi ile tanı konuldu. Ek kardiyak anomaliler periferik pulmoner darlık, patent duktus arteriyozus, Fallot tetralojisi, atriyal septal defekt, ventriküler septal defekt ve kesintili aortik ark tip B idi. Bir hasta Trizomi 9p sendromlu iken, diğeri diyabetik bir annenin bebeği idi. Üç hasta klinik izleme alındı, diğer üç hasta ameliyat edildi.So nuç: Ekokardiyografi ile ortaya konduğu üzere, koroner sinüsün geniş olduğu, koroner sinüs akımının arttığı ve kalıcı sol SVK'nin görüldüğü olgularda sağ SVK yokluğunun dikkatli bir şekilde araştırılması gerekmektedir

Anahtar Kelime:

Konular: Kalp ve Kalp Damar Sistemi Cerrahi

Normal atriyal bağlantılı kalıcı sol superior vena kava ile birlikte sağ superior vena kava yokluğu

Öz:

Background: This study aims to investigate the role of echocardiography in the detection of venous anomalies of large thoracic veins in patients with large coronary sinus. Methods: Between January 2010 and March 2012, six patients (3 boys, 3 girls; mean age 4.1; range 3 days - 9 years) were diagnosed with an absent right superior vena cava (RSVC) accompanied by persistent left superior vena cava (PLSVC) in our clinic. The diagnosis of the absent RSVC was established by echocardiography and angiography. Results: Diagnosis of the absent RSVC was confirmed by echocardiography in four patients. The diagnosis was based on cardiac catheterization and angiography in two patients. Additional cardiac anomalies included peripheral pulmonary stenosis, patent ductus arteriosus, tetralogy of Fallot, atrial septal defect, ventricular septal defect and interrupted aortic arch type B. One patient had Trisomy 9p syndrome, while another one was the baby of a diabetic mother. Three patients were followed clinically, while other three patients were operated. Conclusion: Absent RSVC should be thoroughly investigated in cases with a large coronary sinus along with increased coronary sinus flow and PLSVC, as evidenced by echocardiography

Anahtar Kelime:

Konular: Kalp ve Kalp Damar Sistemi Cerrahi

Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık

1. Irlich G, Herzer JA, Schulte HD, Irnich W. Left persisting, singular superior vena cava and pacemaker electrode implantation by right cephalic vein. Z Kardiol 1976;65:575- 82. [Abstract]
2. Lenox CC, Zuberbuhler JR, Park SC, Neches WH, Mathews RA, Fricker FJ, et al. Absent right superior vena cava with persistent left superior vena cava: implications and management. Am J Cardiol 1980;45:117-22.
3. Geva T, Praagh ST. Abnormal systemic venous connections. In: Allen HD, Driscoll DJ, Shaddy RE, Feltes TF, editors. Moss and Adams' heart disease in infants, children, and adolescents: including the fetus and young adults. 7th ed. Philadelphia: Lippincott Williams & Wilkins; 2008. p. 793-816.
4. Erdoğan M, Karakaş P, Uygur F, Meşe B, Yamak B, Bozkir MG. Persistent left superior vena cava: the anatomical and surgical importance. West Indian Med J 2007;56:72-6.
5. Chandra A, Reul GJ Jr. Persistent left superior vena cava discovered during placement of central venous catheter. Tex Heart Inst J 1998;25:90.
6. Bartram U, Van Praagh S, Levine JC, Hines M, Bensky AS, Van Praagh R. Absent right superior vena cava in visceroatrial situs solitus. Am J Cardiol 1997;80:175-83.
7. Huang SK. Persistent left superior vena cava in a man with ventricular fibrillation. Chest 1986;89:155-7.
8. Korkmaz L, Akyüz AR, Erkuş ME, Topal C. Isolated persistent left superior vena cava with absent right superior vena cava in two cases. Turk Kardiyol Dern Ars 2011;39:501-4.

APA	CEYLAN Ö, Ozgur S, ÖRÜN U, Doğan V, KOÇ M, Yilmaz O, Keskin M, karademir s (2014). Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. , 7 - 12.
Chicago	CEYLAN Özben,Ozgur Senem,ÖRÜN Utku Arman,Doğan Vehbi,KOÇ Murat,Yilmaz Osman,Keskin Mahmut,karademir selmin Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. (2014): 7 - 12.
MLA	CEYLAN Özben,Ozgur Senem,ÖRÜN Utku Arman,Doğan Vehbi,KOÇ Murat,Yilmaz Osman,Keskin Mahmut,karademir selmin Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. , 2014, ss.7 - 12.
AMA	CEYLAN Ö,Ozgur S,ÖRÜN U,Doğan V,KOÇ M,Yilmaz O,Keskin M,karademir s Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. . 2014; 7 - 12.
Vancouver	CEYLAN Ö,Ozgur S,ÖRÜN U,Doğan V,KOÇ M,Yilmaz O,Keskin M,karademir s Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. . 2014; 7 - 12.
IEEE	CEYLAN Ö,Ozgur S,ÖRÜN U,Doğan V,KOÇ M,Yilmaz O,Keskin M,karademir s "Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement." , ss.7 - 12, 2014.
ISNAD	CEYLAN, Özben vd. "Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement". (2014), 7-12.

APA	CEYLAN Ö, Ozgur S, ÖRÜN U, Doğan V, KOÇ M, Yilmaz O, Keskin M, karademir s (2014). Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. Türk Göğüs Kalp Damar Cerrahisi Dergisi, 22(1), 7 - 12.
Chicago	CEYLAN Özben,Ozgur Senem,ÖRÜN Utku Arman,Doğan Vehbi,KOÇ Murat,Yilmaz Osman,Keskin Mahmut,karademir selmin Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. Türk Göğüs Kalp Damar Cerrahisi Dergisi 22, no.1 (2014): 7 - 12.
MLA	CEYLAN Özben,Ozgur Senem,ÖRÜN Utku Arman,Doğan Vehbi,KOÇ Murat,Yilmaz Osman,Keskin Mahmut,karademir selmin Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. Türk Göğüs Kalp Damar Cerrahisi Dergisi, vol.22, no.1, 2014, ss.7 - 12.
AMA	CEYLAN Ö,Ozgur S,ÖRÜN U,Doğan V,KOÇ M,Yilmaz O,Keskin M,karademir s Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. Türk Göğüs Kalp Damar Cerrahisi Dergisi. 2014; 22(1): 7 - 12.
Vancouver	CEYLAN Ö,Ozgur S,ÖRÜN U,Doğan V,KOÇ M,Yilmaz O,Keskin M,karademir s Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement. Türk Göğüs Kalp Damar Cerrahisi Dergisi. 2014; 22(1): 7 - 12.
IEEE	CEYLAN Ö,Ozgur S,ÖRÜN U,Doğan V,KOÇ M,Yilmaz O,Keskin M,karademir s "Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement." Türk Göğüs Kalp Damar Cerrahisi Dergisi, 22, ss.7 - 12, 2014.
ISNAD	CEYLAN, Özben vd. "Absent right superior vena cava with persistent left superior vena cava and normal atrial arrangement". Türk Göğüs Kalp Damar Cerrahisi Dergisi 22/1 (2014), 7-12.