İntrodoction: Cystic hydatid disease is a parasitic infestation caused by Echinococcus Granulosus, usually affecting liver and lungs, with rare involvement of other organs. It is common in underdeveloped and developing countries. In clinical course of the disease, isolated spleen involvement is very rare. Case presentation: Our case; 64-year-old male patient had complaints about colicky abdominal pain getting severe with time in the left upper quadrant and in the epigastric region, nausea and vomiting. In the radiological viewing of the patient, isolated hydatid cyst was detected. Following the preoperative preparations, the patient was taken into operation and splenectomy surgery was performed. In the postoperative follow-ups, no pathological findings were observed. It was followed by albendazole treatment. In the long period follow-ups, no pathological findings were detected.