Yıl: 2017 Cilt: 15 Sayı: 1 Sayfa Aralığı: 47 - 50 Metin Dili: İngilizce DOI: 10.4274/jcp.03371 İndeks Tarihi: 03-12-2018

Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome

Öz:
Anomalous origin of the left coronary artery arising from pulmonary arteryALCAPA syndrome is a rare congenital heart disease seen in children. If untreated,it may lead to congestive heart failure, dilated cardiomyopathy (DCM), ischemicand arrhythmic complications may lead to patient’s death. ALCAPA is diagnosedwith echocardiography; in the patients of suspected diagnosis, computerizedtomography, magnetic resonance imaging and cardiac catheterization are used forfurther testing. Surgically correctable ALCAPA syndrome must be considered asetiology of DCM in children. In this report, we presented the case of an infant that wasreferred to our center with the diagnosis of DCM, who was echocardiographicallydiagnosed with ALCAPA syndrome and successfully treated with surgery, as wellas a review of recent literature.
Anahtar Kelime:

Konular: Tıbbi Etik Pediatri

Süt Çocuğunda Kalp Yetersizliği ile Başvuran Dilate Kardiyomiyopatinin Düzeltilebilir Bir Nedeni: ALCAPA Sendromu

Öz:
Sol koroner arterin pulmoner arterden çıkış anomalisi olarak tanımlanan ALCAPA sendromu, çocuklarda nadir görülen bir konjenital kalp hastalığıdır. Tedavi edilmediği zaman konjestif kalp yetmezliği, dilate kardiyomiyopati (DKM), iskemik ve aritmik komplikasyonlarla hasta kaybedilebilir. Tanı ekokardiyografi bulgularıyla koyulur, tanıdan şüphelenilen olgularda bilgisayarlı tomografi, manyetik rezonans görüntüleme ve kalp kateterizasyonu gibi ileri tetkiklerden faydalanılabilir. Çocukluk çağında DKM tanısı alan hastalarda etiyolojide, cerrahi olarak düzeltme şansı olan ALCAPA sendromu mutlaka düşünülmelidir. Bu yazıda, merkezimize DKM tanısıyla sevk edilen, ekokardiyografi ile ALCAPA sendromu tanısı konulup, başarılı cerrahi tamir yapılan hasta olgu sunumu yapıldı ve son literatür gözden geçirildi.
Anahtar Kelime:

Konular: Tıbbi Etik Pediatri
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
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APA güvenç o, SAYGI M, ozturk e, GÜZELTAŞ A (2017). Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. , 47 - 50. 10.4274/jcp.03371
Chicago güvenç osman,SAYGI Murat,ozturk erkut,GÜZELTAŞ Alper Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. (2017): 47 - 50. 10.4274/jcp.03371
MLA güvenç osman,SAYGI Murat,ozturk erkut,GÜZELTAŞ Alper Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. , 2017, ss.47 - 50. 10.4274/jcp.03371
AMA güvenç o,SAYGI M,ozturk e,GÜZELTAŞ A Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. . 2017; 47 - 50. 10.4274/jcp.03371
Vancouver güvenç o,SAYGI M,ozturk e,GÜZELTAŞ A Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. . 2017; 47 - 50. 10.4274/jcp.03371
IEEE güvenç o,SAYGI M,ozturk e,GÜZELTAŞ A "Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome." , ss.47 - 50, 2017. 10.4274/jcp.03371
ISNAD güvenç, osman vd. "Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome". (2017), 47-50. https://doi.org/10.4274/jcp.03371
APA güvenç o, SAYGI M, ozturk e, GÜZELTAŞ A (2017). Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. Güncel Pediatri, 15(1), 47 - 50. 10.4274/jcp.03371
Chicago güvenç osman,SAYGI Murat,ozturk erkut,GÜZELTAŞ Alper Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. Güncel Pediatri 15, no.1 (2017): 47 - 50. 10.4274/jcp.03371
MLA güvenç osman,SAYGI Murat,ozturk erkut,GÜZELTAŞ Alper Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. Güncel Pediatri, vol.15, no.1, 2017, ss.47 - 50. 10.4274/jcp.03371
AMA güvenç o,SAYGI M,ozturk e,GÜZELTAŞ A Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. Güncel Pediatri. 2017; 15(1): 47 - 50. 10.4274/jcp.03371
Vancouver güvenç o,SAYGI M,ozturk e,GÜZELTAŞ A Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome. Güncel Pediatri. 2017; 15(1): 47 - 50. 10.4274/jcp.03371
IEEE güvenç o,SAYGI M,ozturk e,GÜZELTAŞ A "Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome." Güncel Pediatri, 15, ss.47 - 50, 2017. 10.4274/jcp.03371
ISNAD güvenç, osman vd. "Correctable Cause of Dilated Cardiomyopathy in an Infant with Heart Failure: ALCAPA Syndrome". Güncel Pediatri 15/1 (2017), 47-50. https://doi.org/10.4274/jcp.03371