Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy

Canan ALTAY, ((T.A.), Dokuz Eylül University School of Medicine,)
Mustafa SEÇİL, ((T.A.), Dokuz Eylül University School of Medicine,)
Tevfik DEMİR, ((T.A.), Dokuz Eylül University School of Medicine,)
Tahir ATİK, ((T.A.), Dokuz Eylül University School of Medicine,)
Gülçin AKINCI, ((T.A.), Dokuz Eylül University School of Medicine,)
Nilüfer Özdemir KUTBAY, ((T.A.), Dokuz Eylül University School of Medicine,)
Ela Keskin TEMELOĞLU, ((T.A.), Dokuz Eylül University School of Medicine,)
Ilgın Yıldırım ŞİMŞİR, ((T.A.), Dokuz Eylül University School of Medicine,)
Seçil ÖZIŞIK, ((T.A.), Dokuz Eylül University School of Medicine,)
Leyla DEMİR, ((T.A.), Dokuz Eylül University School of Medicine,)
Erdal EREN,
Emine Burçin TUNA,
Hasibe AYTAÇ,
Hüseyin ONAY,
Barış AKINCI,
Diagnostic and Interventional Radiology
2 1
Yıl: 2017 Cilt: 23 Sayı: 6 Sayfa Aralığı: 428 - 434 Metin Dili: İngilizce İndeks Tarihi: 29-07-2022

Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy

Öz:
PURPOSEWe aimed to investigate residual adipose tissue with whole-body magnetic resonance imagingto differentiate between subtypes of lipodystrophy.METHODSA total of 32 patients (12 with congenital generalized lipodystrophy [CGL], 1 with acquired generalizedlipodystrophy [AGL], 12 with familial partial lipodystrophy [FPLD], and 7 with acquiredpartial lipodystrophy [APL]) were included.RESULTSDespite generalized loss of metabolically active adipose tissue, patients with CGL1 caused byAGPAT2 mutations had a significant amount of residual adipose tissue in the scalp, earlobes, retro-orbitalregion, and palms and soles. No residual adipose tissue was noted particularly in thehead and neck, palms and soles in CGL2 caused by BSCL2 mutations. CGL4 caused by mutationsin the PTRF gene was characterized with well-preserved retro-orbital and bone marrow fat inthe absence of any visible residual adipose tissue in other areas. No residual adipose tissue wasobserved in AGL. Despite loss of subcutaneous fat, periarticular adipose tissue was preserved inthe lower limbs of patients with FPLD. Retro-orbital adipose tissue was surprisingly preserved inAPL, although they lacked head and neck fat.CONCLUSIONLipodystrophies are a heterogeneous group of disorders characterized by generalized or partialloss of adipose tissue, which can be congenital or acquired. Our results suggest that residualadipose tissue characteristics can help distinguish different subtypes of lipodystrophy
Anahtar Kelime:

Konular: Radyoloji, Nükleer Tıp, Tıbbi Görüntüleme
Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık
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APA ALTAY C, SEÇİL M, DEMİR T, ATIK T, AKINCI G, KUTBAY N, TEMELOĞLU E, YILDIRIM SIMSIR I, ÖZIŞIK S, DEMİR L, Eren E, tuna b, AYTAÇ H, ONAY H, AKINCI B (2017). Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. , 428 - 434.
Chicago ALTAY Canan,SEÇİL Mustafa,DEMİR Tevfik,ATIK TAHIR,AKINCI Gülçin,KUTBAY Nilüfer Özdemir,TEMELOĞLU Ela Keskin,YILDIRIM SIMSIR ILGIN,ÖZIŞIK Seçil,DEMİR LEYLA,Eren Erdal,tuna burçin,AYTAÇ HASİBE,ONAY Hüseyin,AKINCI Barış Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. (2017): 428 - 434.
MLA ALTAY Canan,SEÇİL Mustafa,DEMİR Tevfik,ATIK TAHIR,AKINCI Gülçin,KUTBAY Nilüfer Özdemir,TEMELOĞLU Ela Keskin,YILDIRIM SIMSIR ILGIN,ÖZIŞIK Seçil,DEMİR LEYLA,Eren Erdal,tuna burçin,AYTAÇ HASİBE,ONAY Hüseyin,AKINCI Barış Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. , 2017, ss.428 - 434.
AMA ALTAY C,SEÇİL M,DEMİR T,ATIK T,AKINCI G,KUTBAY N,TEMELOĞLU E,YILDIRIM SIMSIR I,ÖZIŞIK S,DEMİR L,Eren E,tuna b,AYTAÇ H,ONAY H,AKINCI B Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. . 2017; 428 - 434.
Vancouver ALTAY C,SEÇİL M,DEMİR T,ATIK T,AKINCI G,KUTBAY N,TEMELOĞLU E,YILDIRIM SIMSIR I,ÖZIŞIK S,DEMİR L,Eren E,tuna b,AYTAÇ H,ONAY H,AKINCI B Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. . 2017; 428 - 434.
IEEE ALTAY C,SEÇİL M,DEMİR T,ATIK T,AKINCI G,KUTBAY N,TEMELOĞLU E,YILDIRIM SIMSIR I,ÖZIŞIK S,DEMİR L,Eren E,tuna b,AYTAÇ H,ONAY H,AKINCI B "Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy." , ss.428 - 434, 2017.
ISNAD ALTAY, Canan vd. "Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy". (2017), 428-434.
APA ALTAY C, SEÇİL M, DEMİR T, ATIK T, AKINCI G, KUTBAY N, TEMELOĞLU E, YILDIRIM SIMSIR I, ÖZIŞIK S, DEMİR L, Eren E, tuna b, AYTAÇ H, ONAY H, AKINCI B (2017). Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. Diagnostic and Interventional Radiology, 23(6), 428 - 434.
Chicago ALTAY Canan,SEÇİL Mustafa,DEMİR Tevfik,ATIK TAHIR,AKINCI Gülçin,KUTBAY Nilüfer Özdemir,TEMELOĞLU Ela Keskin,YILDIRIM SIMSIR ILGIN,ÖZIŞIK Seçil,DEMİR LEYLA,Eren Erdal,tuna burçin,AYTAÇ HASİBE,ONAY Hüseyin,AKINCI Barış Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. Diagnostic and Interventional Radiology 23, no.6 (2017): 428 - 434.
MLA ALTAY Canan,SEÇİL Mustafa,DEMİR Tevfik,ATIK TAHIR,AKINCI Gülçin,KUTBAY Nilüfer Özdemir,TEMELOĞLU Ela Keskin,YILDIRIM SIMSIR ILGIN,ÖZIŞIK Seçil,DEMİR LEYLA,Eren Erdal,tuna burçin,AYTAÇ HASİBE,ONAY Hüseyin,AKINCI Barış Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. Diagnostic and Interventional Radiology, vol.23, no.6, 2017, ss.428 - 434.
AMA ALTAY C,SEÇİL M,DEMİR T,ATIK T,AKINCI G,KUTBAY N,TEMELOĞLU E,YILDIRIM SIMSIR I,ÖZIŞIK S,DEMİR L,Eren E,tuna b,AYTAÇ H,ONAY H,AKINCI B Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. Diagnostic and Interventional Radiology. 2017; 23(6): 428 - 434.
Vancouver ALTAY C,SEÇİL M,DEMİR T,ATIK T,AKINCI G,KUTBAY N,TEMELOĞLU E,YILDIRIM SIMSIR I,ÖZIŞIK S,DEMİR L,Eren E,tuna b,AYTAÇ H,ONAY H,AKINCI B Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy. Diagnostic and Interventional Radiology. 2017; 23(6): 428 - 434.
IEEE ALTAY C,SEÇİL M,DEMİR T,ATIK T,AKINCI G,KUTBAY N,TEMELOĞLU E,YILDIRIM SIMSIR I,ÖZIŞIK S,DEMİR L,Eren E,tuna b,AYTAÇ H,ONAY H,AKINCI B "Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy." Diagnostic and Interventional Radiology, 23, ss.428 - 434, 2017.
ISNAD ALTAY, Canan vd. "Determining residual adipose tissue characteristics with MRI in patients with various subtypes of lipodystrophy". Diagnostic and Interventional Radiology 23/6 (2017), 428-434.
Sayfa Oluşturulma Tarihi
23-04-2024 6:37

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