EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES
Yıl: 2018 Cilt: 20 Sayı: 3 Sayfa Aralığı: 353 - 357 Metin Dili: İngilizce DOI: 10.24938/kutfd.442281 İndeks Tarihi: 04-09-2019
EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES
Öz: Ectodermal dysplasia (ED) is a group of congenital anomalies characterized by defects of two or more ectoderm-derived structures, such as hair, teeth and nails. The aim of this paper is to describe the characteristics and prosthodontic treatment of three cases with ED. Case 1: A 6-year-old boy was brought to our clinic with complaint of tooth ageneses. In clinical and radiographical examination, patient presented anodontia of permanent teeth. Medical history revealed that the child has cutaneous dyshidrosis and hypohidrosis. Based on the findings, the patient was diagnosed as Anhydrotic ED. To provide function, fonation and aesthetics, a complete denture for lower jaw and partial denture for upper jaw were made. Case 2-3: Two brothers (aged 8, 9) were broght to our clinic with complaints of dental caries, dental pain and missing teeth. They had a medical history including hypohidrosis and problems with thermoregulation, and both of the patients presented with oligodontia. Based on the findings, brothers were diagnosed as Familial ED. Firstly, extractions and restorations were completed after which partial dentures were made to gain desired function. It is important to note that early prosthetic intervention gives oppurtunity to the child to develop physically, emotionally and socially like other healthy individuals.
Anahtar Kelime: Konular:
Ektodermal Displazili Çocuklarda Erken Protetik Tedavi: Üç Olgu Sunumu
Öz: Ektordermal displazi (ED) saç, diş, tırnak ve tükürük bezleri gibi ektoderm kökenli dokuların iki veya daha fazlasında görülen bozukluk ile karakterize konjenital bir anomalidir. Bu makalenin amacı; ED görülen üç hastanın klinik bulgularını ve protetik tedavilerini anlatmaktır. Olgu 1: 6 yaşındaki erkek hasta diş eksikliği şikayeti ile kliniğimize başvurmuştur. Yapılan klinik ve radyografik muayenede, hastanın daimi dişlerinde anadonti olduğu tespit edilmiştir. Hastanın medikal hikayesinde, kutanöz dishidrozis ve hipohidroz olduğu öğrenilmiştir. Bu bulgular sonucunda, hastaya anhidrotik ED tanısı konulmuştur. Fonksiyon, fonasyon ve estetiğin sağlanması amacıyla alt çeneye total protez, üst çeneye ise parsiyel protez yapılmıştır. Olgu 2-3: İki erkek kardeş hasta (yaş 8 ve 9) diş çürüğü, diş ağrısı ve diş eksikliği şikayetleri ile kliniğimize başvurmuştur. Medikal hikayelerinden, hipohidrozis ve termoregülasyon gibi problemlere sahip olduğu öğrenilmiştir ve her iki hastada da oligodonti görülmüştür. Bu bulgular ışığında, kardeşlere Ailesel ED tanısı konulmuştur. Öncelikle hastaların çekim ve restorasyonları tamamlanmıştır. Ardından istenen fonksiyonun geri kazandırılması amacıyla parsiyel protezler yapılmıştır. Erken protetik tedavilerin bu hastalarda, diğer sağlıklı bireyler gibi fiziksel, duygusal ve sosyal açıdan gelişmeleri için fırsat oluşturduğu unutulmamalıdır.
Anahtar Kelime: Konular:
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
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| APA | Tulumbacı F, sert t, ERKMEN ALMAZ M (2018). EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. , 353 - 357. 10.24938/kutfd.442281 |
| Chicago | Tulumbacı Fatih,sert tuğba,ERKMEN ALMAZ MERVE EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. (2018): 353 - 357. 10.24938/kutfd.442281 |
| MLA | Tulumbacı Fatih,sert tuğba,ERKMEN ALMAZ MERVE EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. , 2018, ss.353 - 357. 10.24938/kutfd.442281 |
| AMA | Tulumbacı F,sert t,ERKMEN ALMAZ M EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. . 2018; 353 - 357. 10.24938/kutfd.442281 |
| Vancouver | Tulumbacı F,sert t,ERKMEN ALMAZ M EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. . 2018; 353 - 357. 10.24938/kutfd.442281 |
| IEEE | Tulumbacı F,sert t,ERKMEN ALMAZ M "EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES." , ss.353 - 357, 2018. 10.24938/kutfd.442281 |
| ISNAD | Tulumbacı, Fatih vd. "EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES". (2018), 353-357. https://doi.org/10.24938/kutfd.442281 |
| APA | Tulumbacı F, sert t, ERKMEN ALMAZ M (2018). EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. Kırıkkale Üniversitesi Tıp Fakültesi Dergisi, 20(3), 353 - 357. 10.24938/kutfd.442281 |
| Chicago | Tulumbacı Fatih,sert tuğba,ERKMEN ALMAZ MERVE EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. Kırıkkale Üniversitesi Tıp Fakültesi Dergisi 20, no.3 (2018): 353 - 357. 10.24938/kutfd.442281 |
| MLA | Tulumbacı Fatih,sert tuğba,ERKMEN ALMAZ MERVE EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. Kırıkkale Üniversitesi Tıp Fakültesi Dergisi, vol.20, no.3, 2018, ss.353 - 357. 10.24938/kutfd.442281 |
| AMA | Tulumbacı F,sert t,ERKMEN ALMAZ M EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. Kırıkkale Üniversitesi Tıp Fakültesi Dergisi. 2018; 20(3): 353 - 357. 10.24938/kutfd.442281 |
| Vancouver | Tulumbacı F,sert t,ERKMEN ALMAZ M EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES. Kırıkkale Üniversitesi Tıp Fakültesi Dergisi. 2018; 20(3): 353 - 357. 10.24938/kutfd.442281 |
| IEEE | Tulumbacı F,sert t,ERKMEN ALMAZ M "EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES." Kırıkkale Üniversitesi Tıp Fakültesi Dergisi, 20, ss.353 - 357, 2018. 10.24938/kutfd.442281 |
| ISNAD | Tulumbacı, Fatih vd. "EARLY PROSTHETIC MANAGEMENT OF CHILDREN WITH ECTODERMAL DYSPLASIA: A REPORT OF THREE CASES". Kırıkkale Üniversitesi Tıp Fakültesi Dergisi 20/3 (2018), 353-357. https://doi.org/10.24938/kutfd.442281 |
