Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey

Yılmaz, Ebru; ÖZCAN, Alper; UNAL, Ekrem; ÖZTÜRK, Figen; TURAN, Cüneyt; KARAKÜKCÜ, Musa; Patıroglu, Türkan; Özdemir, Mehmet Akif; COŞKUN, Abdulhakim; IŞIK, Bilgen; akgun, hulya

doi:10.3906/sag-1902-106

Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey

Turkish Journal of Medical Sciences

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Yıl: 2020 Cilt: 50 Sayı: 1 Sayfa Aralığı: 18 - 24 Metin Dili: İngilizce DOI: 10.3906/sag-1902-106 İndeks Tarihi: 27-04-2020

Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey

Öz:

Background/aim: Non-Wilms renal tumors (NWRTs) are rarely encountered in children. The aim of this study is to determine thetreatment strategies, prognosis, outcomes, and survival of children with NWRTs at Erciyes University in Kayseri, Turkey.Materials and methods: Medical records of all patients (n = 20) treated for NWRTs over a 23-year period (1995–2018) were reviewedretrospectively.Results: There was male predominance (female/male: 7/13); the median age at diagnosis was 3.2 years old (0.1–13.5 years old). Themajor histological groups included mesoblastic nephroma (MBN), (n: 5, 25%), malignant rhabdoid tumor (MRT), (n: 5, 25%), renalcell carcinoma, (n: 3, 15%), inflammatory myofibroblastic tumor (n: 2, 10%), multilocular cystic renal tumors (n: 2, 10%), metanephricadenoma (n: 1, 5%), renal neuroblastoma (n: 1, 5%), and bilateral renal Ewing sarcoma/primitive neuroectodermal tumor (ES/PNET)(n: 1, 5%). All of the patients with NWRTs had radical nephrectomy except the child with bilateral renal ES/PNET. Six children diedbecause of progressive disease; the mortality rate was 30% (n: 6).Conclusion: We have made the first report of bilateral renal involvement of ES/PNET in the English medical literature. Physiciansdealing with pediatric renal masses should be alert to the high mortality rate in children with MRT, MBN, and ES/PNET and theyshould design substantial management plans for NWRTs.

Anahtar Kelime:

Konular: Cerrahi

Belge Türü: Makale Makale Türü: Araştırma Makalesi Erişim Türü: Erişime Açık

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APA	UNAL E, Yılmaz E, ÖZCAN A, IŞIK B, KARAKÜKCÜ M, TURAN C, akgun h, ÖZTÜRK F, COŞKUN A, Özdemir M, Patıroglu T (2020). Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. , 18 - 24. 10.3906/sag-1902-106
Chicago	UNAL Ekrem,Yılmaz Ebru,ÖZCAN Alper,IŞIK Bilgen,KARAKÜKCÜ Musa,TURAN Cüneyt,akgun hulya,ÖZTÜRK Figen,COŞKUN Abdulhakim,Özdemir Mehmet Akif,Patıroglu Türkan Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. (2020): 18 - 24. 10.3906/sag-1902-106
MLA	UNAL Ekrem,Yılmaz Ebru,ÖZCAN Alper,IŞIK Bilgen,KARAKÜKCÜ Musa,TURAN Cüneyt,akgun hulya,ÖZTÜRK Figen,COŞKUN Abdulhakim,Özdemir Mehmet Akif,Patıroglu Türkan Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. , 2020, ss.18 - 24. 10.3906/sag-1902-106
AMA	UNAL E,Yılmaz E,ÖZCAN A,IŞIK B,KARAKÜKCÜ M,TURAN C,akgun h,ÖZTÜRK F,COŞKUN A,Özdemir M,Patıroglu T Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. . 2020; 18 - 24. 10.3906/sag-1902-106
Vancouver	UNAL E,Yılmaz E,ÖZCAN A,IŞIK B,KARAKÜKCÜ M,TURAN C,akgun h,ÖZTÜRK F,COŞKUN A,Özdemir M,Patıroglu T Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. . 2020; 18 - 24. 10.3906/sag-1902-106
IEEE	UNAL E,Yılmaz E,ÖZCAN A,IŞIK B,KARAKÜKCÜ M,TURAN C,akgun h,ÖZTÜRK F,COŞKUN A,Özdemir M,Patıroglu T "Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey." , ss.18 - 24, 2020. 10.3906/sag-1902-106
ISNAD	UNAL, Ekrem vd. "Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey". (2020), 18-24. https://doi.org/10.3906/sag-1902-106

APA	UNAL E, Yılmaz E, ÖZCAN A, IŞIK B, KARAKÜKCÜ M, TURAN C, akgun h, ÖZTÜRK F, COŞKUN A, Özdemir M, Patıroglu T (2020). Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. Turkish Journal of Medical Sciences, 50(1), 18 - 24. 10.3906/sag-1902-106
Chicago	UNAL Ekrem,Yılmaz Ebru,ÖZCAN Alper,IŞIK Bilgen,KARAKÜKCÜ Musa,TURAN Cüneyt,akgun hulya,ÖZTÜRK Figen,COŞKUN Abdulhakim,Özdemir Mehmet Akif,Patıroglu Türkan Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. Turkish Journal of Medical Sciences 50, no.1 (2020): 18 - 24. 10.3906/sag-1902-106
MLA	UNAL Ekrem,Yılmaz Ebru,ÖZCAN Alper,IŞIK Bilgen,KARAKÜKCÜ Musa,TURAN Cüneyt,akgun hulya,ÖZTÜRK Figen,COŞKUN Abdulhakim,Özdemir Mehmet Akif,Patıroglu Türkan Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. Turkish Journal of Medical Sciences, vol.50, no.1, 2020, ss.18 - 24. 10.3906/sag-1902-106
AMA	UNAL E,Yılmaz E,ÖZCAN A,IŞIK B,KARAKÜKCÜ M,TURAN C,akgun h,ÖZTÜRK F,COŞKUN A,Özdemir M,Patıroglu T Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. Turkish Journal of Medical Sciences. 2020; 50(1): 18 - 24. 10.3906/sag-1902-106
Vancouver	UNAL E,Yılmaz E,ÖZCAN A,IŞIK B,KARAKÜKCÜ M,TURAN C,akgun h,ÖZTÜRK F,COŞKUN A,Özdemir M,Patıroglu T Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey. Turkish Journal of Medical Sciences. 2020; 50(1): 18 - 24. 10.3906/sag-1902-106
IEEE	UNAL E,Yılmaz E,ÖZCAN A,IŞIK B,KARAKÜKCÜ M,TURAN C,akgun h,ÖZTÜRK F,COŞKUN A,Özdemir M,Patıroglu T "Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey." Turkish Journal of Medical Sciences, 50, ss.18 - 24, 2020. 10.3906/sag-1902-106
ISNAD	UNAL, Ekrem vd. "Twenty children with non-Wilms renal tumors from a reference center in Central Anatolia, Turkey". Turkish Journal of Medical Sciences 50/1 (2020), 18-24. https://doi.org/10.3906/sag-1902-106