The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus
Yıl: 2020 Cilt: 5 Sayı: 1 Sayfa Aralığı: 1 - 6 Metin Dili: İngilizce DOI: DOI: 10.5152/cjms.2020.866 İndeks Tarihi: 21-10-2020
The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus
Öz: BACKGROUND/AIMSPrimary antibody deficiencies (PADs) are the most common group of primary immunodeficiency disorders that present with a widerange of clinical features. We conducted this study to evaluate the frequency and characteristics of patients with PADs.MATERIAL and METHODSThe medical records of 160 children (M:F 99:61, mean age 42.39±28.44 months) were retrospectively reviewed from the Near EastUniversity Hospital database. Children who had PADs were then compared according to their demographic, clinical, and laboratoryfindings.RESULTSA total of 97 children were diagnosed with PADs (49 THGI, 31 IgGD, 1 SIgAD, 8 CVID, 6 IgMD, and 2 PHGI)*. Patients with THGI had theyoungest age at the time of diagnosis (27±16.40 months), and those with CVID had the oldest age at the time of diagnosis (81.62±49.9months old) compared with children in other PAD groups. In the HGG group, 63.9% of children presented with both recurrent wheezing/cough and infections, 22.7% had only recurrent infection, 13.4% of them had only recurrent wheezing/cough, and 71.7% of the childrenwere atopic. At the end of the 2-year follow-up period, 8 patients (5 THGI and 3 IgGSD) out of 70 with HGG recovered.CONCLUSIONPADs generally present with recurrent infections and/or recurrent bronchoconstriction unresponsive to standard asthma treatment.Evaluation of the immune system is important to increase the quality of life of these patients and also decrease the healthcare costs.
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| APA | YURUKER O, sanlidag b, Bahceciler N (2020). The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. , 1 - 6. DOI: 10.5152/cjms.2020.866 |
| Chicago | YURUKER OZEL,sanlidag burcin,Bahceciler Nerin Nadir The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. (2020): 1 - 6. DOI: 10.5152/cjms.2020.866 |
| MLA | YURUKER OZEL,sanlidag burcin,Bahceciler Nerin Nadir The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. , 2020, ss.1 - 6. DOI: 10.5152/cjms.2020.866 |
| AMA | YURUKER O,sanlidag b,Bahceciler N The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. . 2020; 1 - 6. DOI: 10.5152/cjms.2020.866 |
| Vancouver | YURUKER O,sanlidag b,Bahceciler N The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. . 2020; 1 - 6. DOI: 10.5152/cjms.2020.866 |
| IEEE | YURUKER O,sanlidag b,Bahceciler N "The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus." , ss.1 - 6, 2020. DOI: 10.5152/cjms.2020.866 |
| ISNAD | YURUKER, OZEL vd. "The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus". (2020), 1-6. https://doi.org/DOI: 10.5152/cjms.2020.866 |
| APA | YURUKER O, sanlidag b, Bahceciler N (2020). The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. Cyprus Journal of Medical Sciences, 5(1), 1 - 6. DOI: 10.5152/cjms.2020.866 |
| Chicago | YURUKER OZEL,sanlidag burcin,Bahceciler Nerin Nadir The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. Cyprus Journal of Medical Sciences 5, no.1 (2020): 1 - 6. DOI: 10.5152/cjms.2020.866 |
| MLA | YURUKER OZEL,sanlidag burcin,Bahceciler Nerin Nadir The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. Cyprus Journal of Medical Sciences, vol.5, no.1, 2020, ss.1 - 6. DOI: 10.5152/cjms.2020.866 |
| AMA | YURUKER O,sanlidag b,Bahceciler N The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. Cyprus Journal of Medical Sciences. 2020; 5(1): 1 - 6. DOI: 10.5152/cjms.2020.866 |
| Vancouver | YURUKER O,sanlidag b,Bahceciler N The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus. Cyprus Journal of Medical Sciences. 2020; 5(1): 1 - 6. DOI: 10.5152/cjms.2020.866 |
| IEEE | YURUKER O,sanlidag b,Bahceciler N "The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus." Cyprus Journal of Medical Sciences, 5, ss.1 - 6, 2020. DOI: 10.5152/cjms.2020.866 |
| ISNAD | YURUKER, OZEL vd. "The Prevalence and Patient Characteristics of Primary Antibody Deficiencies in a Tertiary Care Setting in North Cyprus". Cyprus Journal of Medical Sciences 5/1 (2020), 1-6. https://doi.org/DOI: 10.5152/cjms.2020.866 |
