A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy
Yıl: 2018 Cilt: 7 Sayı: 2 Sayfa Aralığı: 59 - 62 Metin Dili: İngilizce DOI: 10.5505/respircase.201 8.78557 İndeks Tarihi: 25-11-2020
A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy
Öz: Sjögren’s syndrome (SS), which is characterized bylymphocytic infiltration of the exocrine glands, is thesecond most common multisystem autoimmune disease after rheumatoid arthritis. Pulmonary involvement ranges from 9% to 20% and it usually occurs asan airway disease or interstitial lung disease. Pulmonary arterial hypertension (PAH) is a very rare condition in SS. In SS-associated PAH, the functional classof patients is usually World Health Organization(WHO) Class III/IV and there is no specific treatmentregimen. In addition to nonspecific medical treatmentfor PAH, treatment of the underlying disease andsupportive therapy are important. The aim of thismanuscript was to present a case of SS-related PAH(SRP) followed under bosentan and iloprost combination therapy.
Anahtar Kelime: İloprost ve Bosentan Kombinasyon Tedavisi Uygulanan Bir Sjögren Sendromu İlişkili Pulmoner Hipertansiyon Olgusu
Öz: Sjögren Sendromu (SS) ekzokrin glandların lenfositik infiltrasyonu ile karakterize, romatoid artritten sonra ikinci en sık görülen multisitem otoimmün hastalıktır. Pulmoner tutulum %9-20 sıklıkta bildirilmiştir ve genellikle hava yolu hastalığı ya da interstisyel akciğer hastalığı şeklinde görülür. Pulmoner Arteriyel Hipertansiyon (PAH) gelişimi SS’da çok nadir bir durumdur. SS ilişkili PAH’da hastalar genellikle fonksiyonel sınıf WHO-III/IV’dür ve spesifik bir tedavi rejimi yoktur. PAH’ın nonspesifik tedavisine ek olarak altta yatan hastalığın tedavisi önemlidir. Bu yazıdaki amacımız iloprost ve bosentan kombinasyon tedavisi altında izlediğimiz bir SS ilişkili PAH (SİP) olgusunu takdim etmektir.
Anahtar Kelime: Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
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| APA | demir baha a, EKİCİ B, Ogan N, AKPINAR E (2018). A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. , 59 - 62. 10.5505/respircase.201 8.78557 |
| Chicago | demir baha ayse,EKİCİ Berkay,Ogan Nalan,AKPINAR Eylem Evrim A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. (2018): 59 - 62. 10.5505/respircase.201 8.78557 |
| MLA | demir baha ayse,EKİCİ Berkay,Ogan Nalan,AKPINAR Eylem Evrim A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. , 2018, ss.59 - 62. 10.5505/respircase.201 8.78557 |
| AMA | demir baha a,EKİCİ B,Ogan N,AKPINAR E A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. . 2018; 59 - 62. 10.5505/respircase.201 8.78557 |
| Vancouver | demir baha a,EKİCİ B,Ogan N,AKPINAR E A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. . 2018; 59 - 62. 10.5505/respircase.201 8.78557 |
| IEEE | demir baha a,EKİCİ B,Ogan N,AKPINAR E "A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy." , ss.59 - 62, 2018. 10.5505/respircase.201 8.78557 |
| ISNAD | demir baha, ayse vd. "A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy". (2018), 59-62. https://doi.org/10.5505/respircase.201 8.78557 |
| APA | demir baha a, EKİCİ B, Ogan N, AKPINAR E (2018). A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. Respiratory Case Reports, 7(2), 59 - 62. 10.5505/respircase.201 8.78557 |
| Chicago | demir baha ayse,EKİCİ Berkay,Ogan Nalan,AKPINAR Eylem Evrim A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. Respiratory Case Reports 7, no.2 (2018): 59 - 62. 10.5505/respircase.201 8.78557 |
| MLA | demir baha ayse,EKİCİ Berkay,Ogan Nalan,AKPINAR Eylem Evrim A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. Respiratory Case Reports, vol.7, no.2, 2018, ss.59 - 62. 10.5505/respircase.201 8.78557 |
| AMA | demir baha a,EKİCİ B,Ogan N,AKPINAR E A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. Respiratory Case Reports. 2018; 7(2): 59 - 62. 10.5505/respircase.201 8.78557 |
| Vancouver | demir baha a,EKİCİ B,Ogan N,AKPINAR E A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy. Respiratory Case Reports. 2018; 7(2): 59 - 62. 10.5505/respircase.201 8.78557 |
| IEEE | demir baha a,EKİCİ B,Ogan N,AKPINAR E "A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy." Respiratory Case Reports, 7, ss.59 - 62, 2018. 10.5505/respircase.201 8.78557 |
| ISNAD | demir baha, ayse vd. "A Case of Sjögren’s Syndrome-Related Pulmonary Arterial Hypertension Treated with Iloprost and Bosentan Combination Therapy". Respiratory Case Reports 7/2 (2018), 59-62. https://doi.org/10.5505/respircase.201 8.78557 |
