Yıl: 2022 Cilt: 50 Sayı: 1 Sayfa Aralığı: 72 - 74 Metin Dili: İngilizce DOI: 10.5152/TJAR.2021.1273 İndeks Tarihi: 22-06-2022

Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report

Öz:
West syndrome is a rare syndrome that consists of a triad of infantile spasms, hypsarrhythmia pattern on electroencephalogram and mental retardation. Tuberous sclerosis complex (TSC) is one of the disorders that can cause it. Radiology suites are considered as remote locations for anaesthesiologists, and the delivery of anaesthesia becomes challenging if a patient with such a rare disease having multiple anaesthetic implications arrives. We present anaesthetic management for the radiological procedure of the MRI brain of a year old paediatric patient with the West syndrome having suspected TSC based on presenting signs and symptoms. Anaesthetic consideration and management of this rare syndrome are discussed. Detailed preoperative assessment, pre-emptive preparation for possible difficult intubation and difficult intravenous access, careful positioning and prevention of seizures should be the goal. Thorough knowledge of the disease process, its manifestation and its management is the key to the successful management of such cases.
Anahtar Kelime:

Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
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APA Dhanani M, Ul Haq M (2022). Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. , 72 - 74. 10.5152/TJAR.2021.1273
Chicago Dhanani Malika Hameed,Ul Haq Muhammad Irfan Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. (2022): 72 - 74. 10.5152/TJAR.2021.1273
MLA Dhanani Malika Hameed,Ul Haq Muhammad Irfan Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. , 2022, ss.72 - 74. 10.5152/TJAR.2021.1273
AMA Dhanani M,Ul Haq M Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. . 2022; 72 - 74. 10.5152/TJAR.2021.1273
Vancouver Dhanani M,Ul Haq M Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. . 2022; 72 - 74. 10.5152/TJAR.2021.1273
IEEE Dhanani M,Ul Haq M "Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report." , ss.72 - 74, 2022. 10.5152/TJAR.2021.1273
ISNAD Dhanani, Malika Hameed - Ul Haq, Muhammad Irfan. "Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report". (2022), 72-74. https://doi.org/10.5152/TJAR.2021.1273
APA Dhanani M, Ul Haq M (2022). Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. Turkish Journal of Anaesthesiology and Reanimation, 50(1), 72 - 74. 10.5152/TJAR.2021.1273
Chicago Dhanani Malika Hameed,Ul Haq Muhammad Irfan Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. Turkish Journal of Anaesthesiology and Reanimation 50, no.1 (2022): 72 - 74. 10.5152/TJAR.2021.1273
MLA Dhanani Malika Hameed,Ul Haq Muhammad Irfan Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. Turkish Journal of Anaesthesiology and Reanimation, vol.50, no.1, 2022, ss.72 - 74. 10.5152/TJAR.2021.1273
AMA Dhanani M,Ul Haq M Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. Turkish Journal of Anaesthesiology and Reanimation. 2022; 50(1): 72 - 74. 10.5152/TJAR.2021.1273
Vancouver Dhanani M,Ul Haq M Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report. Turkish Journal of Anaesthesiology and Reanimation. 2022; 50(1): 72 - 74. 10.5152/TJAR.2021.1273
IEEE Dhanani M,Ul Haq M "Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report." Turkish Journal of Anaesthesiology and Reanimation, 50, ss.72 - 74, 2022. 10.5152/TJAR.2021.1273
ISNAD Dhanani, Malika Hameed - Ul Haq, Muhammad Irfan. "Anaesthetic Management of a Child with West Syndrome Associated with Tuberous Sclerosis Complex at a Remote Location: A Case Report". Turkish Journal of Anaesthesiology and Reanimation 50/1 (2022), 72-74. https://doi.org/10.5152/TJAR.2021.1273