LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT

ÇAKÇAK, Devrim Sakallı; GÜN, Taylan; BOZTEPE, Osman Fatih

LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT

Taylan GÜN, (Bahçeşehir Üniversitesi)

Osman Fatih BOZTEPE, (İstinye University, Faculty of Medicine)

Devrim Sakallı ÇAKÇAK (Antalya Medical Park Hospital, Antalya, Turkey)

ENTcase

3 0

Yıl: 2018 Cilt: 4 Sayı: 1 Sayfa Aralığı: 27 - 30 Metin Dili: İngilizce İndeks Tarihi: 21-10-2019

LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT

Öz:

Pemphigus vulgaris (PV) is a rare autoimmun disease characterized by clinically blistering of the skin and mucosa as a result of IgG antibodies against desmosomal proteins of squamous epithelia. 56-yearold male patient was referred to our clinic with the complaints of shortness of breath, hoarseness, dysphagia and throat pain for 3 months and the complaints were intensifying for the last 20 days. Erosive lesions were observed on laryngeal mucosa. Skin biopsy confirmed the diagnosis of pemphigus vulgaris. 1 mg/kg/day dose methylprednisolone was started and at Day 4, the patient’s complaints were subsided. At 7th day, endoscopic laryngeal examination showed completely healed lesions and significant decrease of edema.

Anahtar Kelime:

Konular: Kulak, Burun, Boğaz

BOĞAZ AĞRISI ŞEKLİNDE BULGU VEREN LARİNGEAL PEMFİGUS VULGARİS

Öz:

Pemfigus vulgaris nadir görülen bir otoimmün hastalık olup, skuamoz epitelin desmosomal proteinlerine karşı IgG antikor oluşması sonucu deri ve mukozada büllöz formasyonlarla karakterize bir hastalıktır. 56 yaşında erkek hasta kliniğimize 3 aydır devam eden ve son 20 gündür şiddetlenen nefes darlığı, ses kısıklığı, yutma güçlüğü ve boğaz ağrısı şikayetleri ile başvurdu. Laringeal mukozada eroziv lezyonlar izlendi. Deri biyopsisi ile pemfigus vulgaris tanısı konuldu. 4. Gün 1 mg/kg/gün dozunda metilprednizolon başlandı ve hasta şikayetlerigeriledi.7.Günlaringealmuayenedeödemde ciddi azalma ve tamamen iyileşmiş lezyonlar izlendi.

Anahtar Kelime:

Konular: Kulak, Burun, Boğaz

Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık

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APA	GÜN T, BOZTEPE O, ÇAKÇAK D (2018). LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. , 27 - 30.
Chicago	GÜN Taylan,BOZTEPE Osman Fatih,ÇAKÇAK Devrim Sakallı LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. (2018): 27 - 30.
MLA	GÜN Taylan,BOZTEPE Osman Fatih,ÇAKÇAK Devrim Sakallı LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. , 2018, ss.27 - 30.
AMA	GÜN T,BOZTEPE O,ÇAKÇAK D LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. . 2018; 27 - 30.
Vancouver	GÜN T,BOZTEPE O,ÇAKÇAK D LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. . 2018; 27 - 30.
IEEE	GÜN T,BOZTEPE O,ÇAKÇAK D "LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT." , ss.27 - 30, 2018.
ISNAD	GÜN, Taylan vd. "LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT". (2018), 27-30.

APA	GÜN T, BOZTEPE O, ÇAKÇAK D (2018). LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. ENTcase, 4(1), 27 - 30.
Chicago	GÜN Taylan,BOZTEPE Osman Fatih,ÇAKÇAK Devrim Sakallı LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. ENTcase 4, no.1 (2018): 27 - 30.
MLA	GÜN Taylan,BOZTEPE Osman Fatih,ÇAKÇAK Devrim Sakallı LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. ENTcase, vol.4, no.1, 2018, ss.27 - 30.
AMA	GÜN T,BOZTEPE O,ÇAKÇAK D LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. ENTcase. 2018; 4(1): 27 - 30.
Vancouver	GÜN T,BOZTEPE O,ÇAKÇAK D LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT. ENTcase. 2018; 4(1): 27 - 30.
IEEE	GÜN T,BOZTEPE O,ÇAKÇAK D "LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT." ENTcase, 4, ss.27 - 30, 2018.
ISNAD	GÜN, Taylan vd. "LARYNGEAL PEMPHIGUS VULGARIS PRESENTING AS SORE THROAT". ENTcase 4/1 (2018), 27-30.