Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case
Yıl: 2019 Cilt: 25 Sayı: 3 Sayfa Aralığı: 371 - 374 Metin Dili: İngilizce DOI: 10.5336/dentalsci.2018-64084 İndeks Tarihi: 30-04-2020
Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case
Öz: Williams-Beuren syndrome (WBS) is a genetic disorder, caused by a deletion of chromosome 7. WBS characterized by typical facies and personality, cardiovascular disease, connectivetissue growth and endocrine abnormalities. In the oral cavity, malocclusion, micrognathism, hypodontia, enamel hypoplasia, microdontia are among the wide spectrum of abnormalities identifiedin this disease. In this study, orofacial features of a 14-year-old male patient with WBS were presented. This case, contrary the literature, had multiple supernumerary teeth. The literature was reviewed because of this rare condition.
Anahtar Kelime: Konular:
Williams-Beuren Sendromlu Bir Hastada Multipl Sürmemiş Sürnumere Dişler: Nadir Bir Olgu Sunumu
Öz: Williams Beuren sendromu (WBS) kromozom 7’de mikrodelesyonların neden olduğu genetik bir bozukluktur. WBS kardiyovasküler hastalık, karakteristik fasiyal ve kişilik özellikleri, bağ dokusu büyümesi ve endokrin anormallikleri ile karakterizedir. İntraoral olarak maloklüzyon, mikrognati, hipodonti, mine hipoplazisi ve mikrodonti tespit edilen geniş anomali yelpazesi arasındadır. Bu çalışmada, WBS'li 14 yaşındaki bir erkek hastanın orofasiyal özellikleri sunulmuştur. Bu olguda, literatürün aksine, multipl sürnumere dişler mevcuttur. Nadir görülen olgu hakkında literatür bilgileri yeniden gözden geçirilmiştir.
Anahtar Kelime: Konular:
Belge Türü: Makale Makale Türü: Olgu Sunumu Erişim Türü: Erişime Açık
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| APA | ÇİTİR M, ZENGİN A (2019). Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. , 371 - 374. 10.5336/dentalsci.2018-64084 |
| Chicago | ÇİTİR MESUDE,ZENGİN Ayşe Zeynep Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. (2019): 371 - 374. 10.5336/dentalsci.2018-64084 |
| MLA | ÇİTİR MESUDE,ZENGİN Ayşe Zeynep Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. , 2019, ss.371 - 374. 10.5336/dentalsci.2018-64084 |
| AMA | ÇİTİR M,ZENGİN A Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. . 2019; 371 - 374. 10.5336/dentalsci.2018-64084 |
| Vancouver | ÇİTİR M,ZENGİN A Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. . 2019; 371 - 374. 10.5336/dentalsci.2018-64084 |
| IEEE | ÇİTİR M,ZENGİN A "Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case." , ss.371 - 374, 2019. 10.5336/dentalsci.2018-64084 |
| ISNAD | ÇİTİR, MESUDE - ZENGİN, Ayşe Zeynep. "Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case". (2019), 371-374. https://doi.org/10.5336/dentalsci.2018-64084 |
| APA | ÇİTİR M, ZENGİN A (2019). Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. Türkiye Klinikleri Diş Hekimliği Bilimleri Dergisi, 25(3), 371 - 374. 10.5336/dentalsci.2018-64084 |
| Chicago | ÇİTİR MESUDE,ZENGİN Ayşe Zeynep Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. Türkiye Klinikleri Diş Hekimliği Bilimleri Dergisi 25, no.3 (2019): 371 - 374. 10.5336/dentalsci.2018-64084 |
| MLA | ÇİTİR MESUDE,ZENGİN Ayşe Zeynep Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. Türkiye Klinikleri Diş Hekimliği Bilimleri Dergisi, vol.25, no.3, 2019, ss.371 - 374. 10.5336/dentalsci.2018-64084 |
| AMA | ÇİTİR M,ZENGİN A Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. Türkiye Klinikleri Diş Hekimliği Bilimleri Dergisi. 2019; 25(3): 371 - 374. 10.5336/dentalsci.2018-64084 |
| Vancouver | ÇİTİR M,ZENGİN A Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case. Türkiye Klinikleri Diş Hekimliği Bilimleri Dergisi. 2019; 25(3): 371 - 374. 10.5336/dentalsci.2018-64084 |
| IEEE | ÇİTİR M,ZENGİN A "Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case." Türkiye Klinikleri Diş Hekimliği Bilimleri Dergisi, 25, ss.371 - 374, 2019. 10.5336/dentalsci.2018-64084 |
| ISNAD | ÇİTİR, MESUDE - ZENGİN, Ayşe Zeynep. "Multiple Unerupted and Supernumerary Teeth in a Patient with Williams-Beuren Syndrome: An Unusual Case". Türkiye Klinikleri Diş Hekimliği Bilimleri Dergisi 25/3 (2019), 371-374. https://doi.org/10.5336/dentalsci.2018-64084 |
